Putative poly(U)-specific 3'-to-5' RNA exonuclease%3B involved in 3'-end processing of U6 snRNA removing uridines and generating a terminal 2%26#8242%3B%2C3%26#8242%3B cyclic phosphate%3B essential protein that localizes to the nucleus and mitochondria%3B overexpression suppresses the respiratory defects of oxa1 and mtf2 mutants%3B homolog of S.pombe gene%2C mpn1 and human gene%2C hUSB1%3B mutations in hUSB1 are associated with a rare genodermatosis%2C poikiloderma with neutropenia (OMIM 604173)
